Apical Hypertrophic Cardiomyopathy: A Special Entity.

  • Ajay Adhikaree National Academy of Medical Sciences, Kathmandu, Nepal https://orcid.org/0000-0001-5125-7365
  • Man Bahadur KC Shahid Gangalal National Heart Center, Kathmandu, Nepal
  • Rabi Malla Shahid Gangalal National Heart Center, Kathmandu, Nepal
Keywords: Apical Hypertrophic Cardiomyopathy, Hypertrophic Cardiomyopathy

Abstract

Introduction: Apical Hypertrophic Cardiomyopathy (AHCM) is a unique variant with distinct clinical presentation, genetics, treatment, complications and outcome. Case: A 52 year non-hypertensive Asian male presented with exertional shortness of breath for two years without chest pain, palpitation or syncope. The apex beat was heaving. Electrocardiogram revealed non q wave deep symmetrical T wave inversion in anterolateral leads and echocardiography demonstrated hypertrophied apical septum. Coronary angiogram showed normal coronaries with typical “Ace of Spade” configuration during ventriculography. Conclusion: Characterization of various forms of hypertrophic cardiomyopathy is essential for management purpose as apical hypertrophic cardiomyopathy usually have benign course.

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Author Biographies

Ajay Adhikaree, National Academy of Medical Sciences, Kathmandu, Nepal

DM Cardiology Resident,

National Academy of Medical Sciences, Kathmandu, Nepal.

 

Man Bahadur KC, Shahid Gangalal National Heart Center, Kathmandu, Nepal

Professor,

Department of Cardiology.

 

Rabi Malla, Shahid Gangalal National Heart Center, Kathmandu, Nepal

Professor,

Shahid Gangalal National Heart Center, Kathmandu, Nepal.

 

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Published
2020-01-02
How to Cite
1.
Adhikaree A, KC M, Malla R. Apical Hypertrophic Cardiomyopathy: A Special Entity. J Lumbini Med Coll [Internet]. 2Jan.2020 [cited 2Apr.2020];7(2):116-20. Available from: https://jlmc.edu.np/index.php/JLMC/article/view/296
Section
Case Report